Gene PAH Details
It offers a comprehensive overview of all clinically relevant variants linked to a specified gene. It provides detailed metrics for each variant, including chromosomal position, HGVS c. and p. notation, allele frequencies, carrier rates, and estimated metrics for at-risk couples. By combining gene-level statistics with specific variant-level data, this page enables an in-depth analysis of how particular genes contribute to disease, thus supporting both clinical interpretation and research efforts.
Gene: PAH
Disorder: Hyperphenylalaninemia
Allele Frequency: 0.0167504
Carrier Rate: 0.0329397
Max At-Risk Couples rate: 0.00108502
The table below lists all clinically relevant variants identified in the PAH gene based on the Emirati cohort dataset.
id |
Chromosome Position |
Gene Name |
HGVS c. (Clinically Relevant) |
HGVS p. (Clinically Relevant) |
Allele Count |
Allele Frequency |
18 |
103306564 |
PAH |
NM_000277.3:c.168+5G>C |
p.? |
15 |
0.006281% |
80 |
103248932 |
PAH |
NM_000277.3:c.688G>A |
NP_000268.1:p.Val230Ile |
4 |
0.001675% |
109 |
103234285 |
PAH |
NM_000277.3:c.1208C>T |
NP_000268.1:p.Ala403Val |
3 |
0.001256% |
110 |
103237484 |
PAH |
NM_000277.3:c.1139C>T |
NP_000268.1:p.Thr380Met |
3 |
0.001256% |
182 |
103234270 |
PAH |
NM_000277.3:c.1223G>A |
p.Arg408Gln |
2 |
0.000838% |
183 |
103238211 |
PAH |
NM_000277.3:c.970-2A>G |
|
2 |
0.000838% |
184 |
103245487 |
PAH |
NM_000277.3:c.890G>A |
NP_000268.1:p.Arg297His |
2 |
0.000838% |
185 |
103245488 |
PAH |
NM_000277.3:c.889C>T |
NP_000268.1:p.Arg297Cys |
2 |
0.000838% |
411 |
103234242 |
PAH |
NM_000277.3:c.1251_1252insG |
NP_000268.1:p.Thr418Aspfs*5 |
1 |
0.000419% |
412 |
103237423 |
PAH |
NM_000277.3:c.1199+1G>C |
|
1 |
0.000419% |
413 |
103245479 |
PAH |
NM_000277.3:c.898G>T |
NP_000268.1:p.Ala300Ser |
1 |
0.000419% |
414 |
103246597 |
PAH |
NM_000277.3:c.838G>A |
NP_000268.1:p.Glu280Lys |
1 |
0.000419% |
415 |
103271235 |
PAH |
NM_000277.3:c.441+5G>T |
|
1 |
0.000419% |
416 |
103288534 |
PAH |
NM_000277.3:c.331C>T |
NP_000268.1:p.Arg111Ter |
1 |
0.000419% |
417 |
103306580 |
PAH |
NM_000277.3:c.157C>T |
NP_000268.1:p.Arg53Cys |
1 |
0.000419% |